The case of idiopathic pleuroparenchymal fibroelastosis diagnosed by transbronchial biopsy

Arpag, Huseyin; Sayan, Muhammet; Atilla, Nurhan; Bozkus, Fulsen; Kahraman, Hasan; Bahar, Abdulkadir Yasir; Tokur, Mahmut

doi:10.4103/ejop.ejop_12_18

Huseyin Arpag¹ , Muhammet Sayan² , Nurhan Atilla¹ , Fulsen Bozkus¹ , Hasan Kahraman¹ , Abdulkadir Yasir Bahar³ , Mahmut Tokur²

¹Department of Chest Diseases, Faculty of Medicine, Kahramanmaras Sutcu Imam University, Kahramanmaras, Turkey
²Department of Thoracic Surgery, Faculty of Medicine, Kahramanmaras Sutcu Imam University, Kahramanmaras, Turkey
³Department of Pathology, Faculty of Medicine, Kahramanmaras Sutcu Imam University, Kahramanmaras, Turkey

Eurasian Journal of Pulmonology 2018; 20(2): 104-106 DOI: 10.4103/ejop.ejop_12_18

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Abstract

Pleuroparenchymal fibroelastosis (PPFE) is claasified in idiopathic interstitial pneumonitis group is rarely seen. Etiology and pathophysiology of this entity are not completely understood. The prognosis is poor, and there is no effective treatment except for lung transplantation. Here, we presented a case of PPFE diagnosed by transbronchial biopsy through fiberoptic bronchoscopy and its histopathological and clinicoradiological features.

Keywords: Idiopathic, pleuroparenchymal fibroelastosis, transbronchial biopsy